Asplenia with cardiovascular anomalies

Asplenia with cardiovascular anomalies, also known as Ivemark syndrome and right atrial isomerism, is an example of a heterotaxy syndrome. These uncommon congenital disorders are characterized by defects in the heart, spleen and paired organs such as the lungs and kidneys. Another name is "asplenia-cardiovascular defect-heterotaxy".

Asplenia with cardiovascular anomalies
Other namesIvemark syndrome
This condition is inherited in an autosomal recessive manner
SpecialtyMedical genetics 

Right atrial isomerism is named for its discoverer, Swedish pathologist Biörn Ivemark.

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